What is Hip Dysplasia?
Hip Dysplasia is a comprehensive term that has been used to
include a spectrum of related developmental hip problems in
infants and children, often present at birth. The following are
typical dysplasia problems.
No one knows for sure what causes Hip Dysplasia, but multiple factors are probably
involved.
Incidence is 4 per 1000 live-births in the general population,
but is much more frequent in Lapps and American Indians.
Moreover, the condition tends to run in families and is more
common among girls and firstborns. These facts suggest that
there is a genetic factor involved.
Certain practices such as infant swaddling and use of the
cradle-board in certain cultures increase the chances of
developing hip dysplasia. Hence environmental factors are also
involved.
Added to these is the observation that during the neonatal
period, the baby carries a relatively high level of estrogen
from the mother. This relaxes the ligaments In the body. Some
babies are especially sensitive to the estrogen, thus causing
the hip ligaments to be unduly lax, and the hip "unstable".
The most common symptoms are the pediatrician detecting a "hip
click" during routine post-natal checkup. Actually, a "clunk",
rather than a "click" is detected in the unstable hip, but it
requires experience to tell a "clunk" from a "click". The
pediatrician typically does the Ortolani test by spreading the
thighs, or the Barlow test by bringing the knees together, to
elicit this finding.
In the older infant, the pediatrician may suspect the problem if
the child has tight hip adductors - he has a hard time spreading
the baby’s hips. He may also notice that the skin creases around
the groin or the buttocks are not symmetrical. Or the legs may
appear to be of different lengths.
At age one, the affected child may present with a limp.
Unfortunately, pain is not a problem in the child, hence it is
easy to miss the diagnosis. However, by the time the patient
becomes an adult, arthritic changes will occur, and pain will
set in.
It is difficult to prevent something the cause of which is still
quite elusive. However, it is well known that in cultures that
practice infant swaddling and using cradle boards to carry their
babies, the incidence of hip dysplasia is very high. On the
other hand, cultures that carry their babies astride the
mother’s backs have a low incidence of hip dysplasia. Hence it
appears logical to discourage putting the baby’s legs in the
extended position, and encourage keeping the baby’s hips spread
apart. This latter position places the head of the femur (the
ball) against the acetabulum (the socket), and encourages
deepening of the socket.
It has been recently recognized that certain babies are more
prone to developing hip dysplasia. These "at risk" babies
include the following:
A new procedure can now be used as a screening test to check for
hip dysplasia in the newborn, using an Ultrasound machine. This
is in many ways better than an X-ray examination, which causes
radiation and is notorious for being inaccurate for hip
dysplasia.
The Ultrasound exam can accurately determine the location of the
"ball" in the "socket", the depth of the "socket" and by
stressing the hip during the examination, determine the
stability of the hip as well. By using sound waves rather than
X-rays, there is no risk of radiation to the baby. The
Ultrasound exam had now supplanted X-rays in most instances in
detecting hip dysplasia in newborns, and is now recommended for
all infants "at risk" at around 4 to 6 weeks of age.
After taking a history and performing a physical examination, it
is likely that the doctor will order an Ultrasound examination of the
hips if he/she suspects Hip Dysplasia. As mentioned earlier, this has replaced conventional
X-rays as a way of confirming the diagnosis. Moreover, it is
also a good way of following the progress of the hip with
treatment.
The essence of treatment is to reduce the hip in good position,
and holding it there by positioning. The position of hip
stability is abduction in flexion, and this is the position
often used in treatment.
In the first 4 to 6 months of life, the device used is often a
Pavlik harness. There have been other devices used in the past,
such as the Frejka pillow and the Ilfeld splint, but these are
not used as often these days.
The Pavlik Harness was first introduced by Arnold Pavlik, a
Czech orthopedic surgeon, who first described it in the 1950’s.
Since then, it has become standard treatment for hip dysplasia
in infants. The harness consists of a shoulder harness attached
to foot stirrups that keep the hips in the position of flexion
and abduction, while allowing for a certain degree of movement
within the "safe zone". This allows the femoral head (ball) to
move within limits of safety within the acetabulum (cup), thus
molding and deepening the acetabulum with growth. At birth, the
harness is usually worn full-time for 6 weeks when the hip
stabilizes, followed by another 6 weeks of weaning. If treatment
was started later, or if the hips were more unstable, harness
wear might take longer. Your physician will decide on the
duration of harness treatment. For details on how to care for
your harness, look up The Wheaton-Pavlik Harness: a Guide for
Parents.
In the child beyond 6 months, it may not be possible to reduce
the hip in a Pavlik harness alone. In these cases, the child may
need to be admitted to the hospital and closed reduction
performed under general anesthetic. Sometimes a period of leg
traction may be needed to facilitate the reduction. Following
the reduction, the child is placed in a hip spica cast for about
3 months, followed by the use of a removeable hip abduction
brace for another 3 months after that.
In a child older that 1 year, closed reduction alone may not be
possible. Open reduction becomes necessary. This involves making
an incision to expose the hip at surgery, reducing the hip under
direct vision, and stabilizing the hip by reinforcing the hip
capsule. The child is then placed in a hip spica cast. In some
cases, the hip may redislocate, or continues to stay dysplastic.
At that point, further surgery is needed to reconstruct the hip
(pelvic or femoral osteotomy or both) to stabilize the hip.
After treatment, the Hip Dysplasia in a child discovered to have hip dysplasia within the first
6 weeks of life, that is treatment in a Pavlik harness is successful in
more than 90% of cases. With successful treatment, the hips
develop normally, and no long-term problems need be expected.
For the child discovered to have hip dysplasia later in infancy,
treatment is more prolonged or complicated, but good results
with a normal hip can be expected.
After the age of 1 year, treatment can definitely complicated,
and results more guarded. Multiple operations are not unusual,
and a normal hip may not result.
The untreated hip causes a limp, which is not painful in
childhood. However, arthritis develops early in adult life, and
pain sets in. When pain is severe, joint replacement becomes
necessary.
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